ISSN: 1305-385X
Hakkında: Özel sayılar şeklinde yayınlanır.
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Tuberous Sclerosis, Von Hippel-lindau Disease, Medullary Sponge Kidney, Nephronophthisis/medullary Cystic Disease
Dr. Cihangir AKGÜN,a Dr. Şükrü ARSLANa
aÇocuk Nefroloji BD, Yüzüncü Yıl Üniversitesi Tıp Fakültesi, VAN
Abnormal development of renal parenchyma leads to a multitude of pathologic entities. Abberration of quantitative development leads to renal hypoplasia, whereas disturbances in qualitative development result in dysplasia.
There are numerous disorders that share renal cysts as a common feature like medullary sponge kidney, Tuberous sclerosis complex, Von-Hippel Lindau disease,simple cysts, etc. Herein, Tuberous sclerosis, Von-Hippel Lindau disease, Medullar Sponge Kidney and Nephronophthisis-Medullary Cystic Disease Complex were reviewed with their etiology and pathogenesis, epidemiology, pathology,clinical manifestations, diagnosis and treatmentKeywords: Kistik böbrek hastalıkları; son dönem böbrek yetmezliğiTurkiye Klinikleri J Int Med Sci 2007, 3(21):37-42
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